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H-Abu-OH
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
H-Abu-OH图片
CAS NO:1492-24-6
包装与价格:
包装价格(元)
25g电议
100g电议

产品介绍
H-Abu-OH 是氨基丁酸的三种异构体之一,在患有 Reye 综合征、酪氨酸血症、高胱氨酸尿症、非酮症高甘氨酸血症和鸟氨酸转氨甲酰酶缺乏症的儿童的血浆中升高。
Cas No.1492-24-6
别名L-2-氨基丁酸
化学名(2S)-2-aminobutanoic acid
Canonical SMILESCCC(C(=O)O)N
分子式C4H9NO2
分子量103.1
溶解度Soluble in water or 1% acetic acid
储存条件Desiccate at -20℃
General tipsFor obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while.
Shipping ConditionEvaluation sample solution : ship with blue ice
All other available size: ship with RT , or blue ice upon request
产品描述

H-Abu-OH, one of the three isomers of aminobutyric acid, is elevated in the plasma of children with with Reye's syndrome, tyrosinemia, homocystinuria, nonketotic hyperglycinemia, and ornithine transcarbamylase deficiency.

References:
[1]. Yudkoff M, et al. On the clinical significance of the plasma alpha-amino-n-butyric acid:leucine ratio. Am J Clin Nutr. 1979 Feb;32(2):282-5.