| 包装: | 100 µg |
| 市场价: | 826元 |
| Canonical SMILES | C[N+](C([2H])([2H])[2H])(C)C[C@@H](CC(O)=O)OC(CCCCCCCCCCCCCCCC)=O.[Cl-] |
| 分子式 | C24H45D3NO4• Cl |
| 分子量 | 453.1 |
| 储存条件 | -20°C |
| General tips | For obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while. |
| Shipping Condition | Evaluation sample solution : ship with blue ice All other available size: ship with RT , or blue ice upon request |
| 产品描述 | Heptadecanoyl-L-carnitine-d3is intended for use as an analytical standard for the quantification of heptadecanoyl-L-carnitine by GC- or LC-MS. Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid and L-carnitine . Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmaolnyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.1 1.Malvagia, S., Haynes, C.A., Grisotto, L., et al.Heptadecanoylcarnitine (C17) a novel candidate biomarker for propionic and methylmalonic acidemias during expanded newborn screeningClin. Chim. Acta450342-348(2015) |
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