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D2-羟基戊二酸二乙酯脱氢酶(D2HGDH)抗体
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。

产品名称
D2HGDH蛋白抗体
Anti-D2hgdh
产品介绍
靶标:

D2hgdh


产品别名:

CG3835; D2HGDH; Dmel\CG3835; EG87B1; EG:87B1.3; D2hgdh; D-2-hydroxyglutaric acid dehydrogenase; D-2-hydroxyglutaric acid dehydrogenase; D-2-hydroxyglutaric acid dehydrogenase; CG3835-PA; CG3835-PB; CG3835-PC; D2hgdh-PA; D2hgdh-PB; D2hgdh-PC; D2-羟基戊二酸二乙酯脱氢酶(D2HGDH); D2HGDH蛋白;


背景信息:
This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features.

宿主:Rbt
类型:Pab
同种型:IgG  
应用:WB
纯化方式:亲和纯化
偶联物:Unconjugated
性状:液体
存储溶液:参阅说明书
浓度:Batch dependent (Please refer to the vial label for the specific concentration.)
稀释比例: Optimal dilutions/concentrations should be determined by the end user           
储存:经常使用则4°C保存。-20°C保存不超过两年。避免反复冻融。
注意事项:仅供实验室使用。不适用于人类或动物的任何临床,治疗或诊断用途。不适合动物或人类食用。