植烷酸氧化酶抗体

立即咨询

植烷酸氧化酶抗体

本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。

产品名称

Anti-PHYH
Anti-phytanoyl-CoA 2-hydroxylase Antibody

产品介绍

靶标：

PHYH

产品别名：

LN1； LNAP1； PAHX； PHYH1； RD； PHYH； phytanoyl-CoA 2-hydroxylase； phytanoyl-CoA 2-hydroxylase； phytanoyl-CoA dioxygenase, peroxisomal； phytanic acid oxidase； phytanoil-CoA alpha hydroxylase； phytanoyl-CoA 2 oxoglutarate dioxygenase； phytanoyl-CoA alpha-hydroxylase；植烷酸氧化酶；

背景信息：

This gene is a member of the PhyH family and encodes a peroxisomal protein that is involved in the alpha-oxidation of 3-methyl branched fatty acids. Specifically, this protein converts phytanoyl-CoA to 2-hydroxyphytanoyl-CoA. Mutations in this gene have been associated with Refsum disease (RD) and deficient protein activity has been associated with Zellweger syndrome and rhizomelic chondrodysplasia punctata. Alternate transcriptional splice variants, encoding different isoforms, have been characterized.

宿主：Rbt
类型：Pab
同种型:IgG
应用：WB
纯化方式：亲和纯化
偶联物：Unconjugated
性状：液体
存储溶液：参阅说明书
浓度：Batch dependent (Please refer to the vial label for the specific concentration.)
稀释比例: Optimal dilutions/concentrations should be determined by the end user
储存：经常使用则4°C保存。-20°C保存不超过两年。避免反复冻融。
注意事项：仅供实验室使用。不适用于人类或动物的任何临床，治疗或诊断用途。不适合动物或人类食用。