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长链烯脂酰辅酶A脱氢酶抗体
本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。

产品名称
Anti-HADHA
Anti-hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha Antibody
产品介绍
靶标：

HADHA


产品别名：

ECHA； GBP； HADH； LCEH； LCHAD； MTPA； TP-ALPHA； HADHA； hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha； hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha； trifunctional enzyme subunit alpha, mitochondrial； 3-ketoacyl-Coenzyme A (CoA) thiolase, alpha subunit； 3-oxoacyl-CoA thiolase； 78 kDa gastrin-binding protein； gastrin-binding protein； hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit； hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit； long-chain 2-enoyl-CoA hydratase； long-chain-3-hydroxyacyl-CoA dehydrogenase； mitochondrial long-chain 2-enoyl-Coenzyme A (CoA) hydratase, alpha subunit； mitochondrial long-chain L-3-hydroxyacyl-Coenzyme A (CoA) dehydrogenase, alpha subunit； mitochondrial trifunctional enzyme, alpha subunit； mitochondrial trifunctional protein, alpha subunit； monolysocardiolipin acyltransferase； 长链烯脂酰辅酶A脱氢酶；


背景信息：
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008],

宿主：Rbt
类型：Pab
同种型:IgG  
应用：WB
纯化方式：亲和纯化
偶联物：Unconjugated
性状：液体
存储溶液：参阅说明书
浓度：Batch dependent (Please refer to the vial label for the specific concentration.)
稀释比例: Optimal dilutions/concentrations should be determined by the end user           
储存：经常使用则4°C保存。-20°C保存不超过两年。避免反复冻融。
注意事项：仅供实验室使用。不适用于人类或动物的任何临床，治疗或诊断用途。不适合动物或人类食用。