An internal standard for the quantification of isovaleryl-DL-carnitine
货号:ajcx28210
CAS:2608872-54-2
分子式:C12H15D9NO4 • Cl
分子量：290.8
溶解度:DMF: 15mg/mL,DMSO: 20mg/mL,Ethanol: 25mg/mL,PBS (pH 7.2): 10mg/mL
纯度：98%
存储：Store at -20°C
库存：现货

Background:

Isovaleryl-DL-carnitine-d₉is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine . Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of metabolism characterized by a deficiency in isovaleryl-CoA dehydrogenase.¹

1.Rinaldo, P., Cowan, T.M., and Matern, D.Acylcarnitine profile analysisGenet.Med.10(2)151-156(2008)