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(S)-3,4-Dihydroxybutyric acid
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
(S)-3,4-Dihydroxybutyric acid图片
CAS NO:51267-44-8
包装:10mg
规格:98%
市场价:1069元
分子量:120.1

产品介绍
(S)-3,4-Dihydroxybutyricacid是一种正常的人体尿液代谢物,在琥珀酸半醛脱氢酶(SSADH)缺乏症患者中浓度增加。
CAS:51267-44-8
分子式:C4H8O4
分子量:120.1
纯度:98%
存储:Store at -20°C

Background:

(S)-3,4-Dihydroxybutyric acid is a normal human urinary metabolite that is excreted in increased concentration in patients with succinic semialdehyde dehydrogenase (SSADH) deficiency.




[1]. Shinka T, et al. Rapid and sensitive detection of urinary 4-hydroxybutyric acid and its related compounds by gas chromatography-mass spectrometry in a patient with succinic semialdehyde dehydrogenase deficiency. J Chromatogr B Analyt Technol Biomed Life Sci. 2002 Aug 25;776(1):57-63.