2-Hydroxy-2-methylbutanoic acid 是非正常的代谢物，与羟基戊二酸尿症以及枫糖尿病有关。

2-Hydroxy-2-methylbutyric acid is an unusual metabolite found in the urine of patients with 2-hydroxyglutaric aciduria and maple syrup urine disease.

3739-30-8

C5H10O3

118.132

2-Hydroxy-2-methylbutanoic acid

DMSO:20 mg/mL (169.31 mM)
Powder: -20°C for 3 years
In solvent: -80°C for 2 years