2-Hydroxy-3-methylbutyric acid 是一种 GHB 的结构类似物，其中GHB 是一种中枢神经系统中发现的天然物质，也是一种神经药物。

2-Hydroxy-3-methylbutyric acid (2-hydroxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria, methylmalonic acidemia, propionic acidemia, 3-ketothiolase deficiency, isovaleric acidemia, 3-methylcrotonylglycemia, 3-hydroxy-3-methylglutaric acidemia, multiple carboxylase deficiency, glutaric aciduria, ornithine transcarbamylase deficiency, glyceroluria, tyrosinemia type I, galactosemia, and maple syrup urine disease.

4026-18-0

C5H10O3

118.13

2-Hydroxy-3-methylbutyric acid;2-羟基-3-甲基丁酸;2-Hydroxyisovaleric Acid;(±)-2-Hydroxyisopentanoic Acid;2-Hydroxy-3-methylbutanoic acid

DMSO:194.7 mM
Powder: -20°C for 3 years
In solvent: -80°C for 2 years