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Ethylmalonic acid
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
Ethylmalonic acid图片
CAS NO:601-75-2
包装与价格:
包装价格(元)
500 mg电议
1 g电议

产品名称
乙基丙二酸
2-Ethylmalonic acid
alpha-Carboxybutyrate
产品介绍
Ethylmalonic acid 是潜在有毒物质,非致癌性,与神经性厌食和甲氧基脱羧酶缺乏症有关。

产品描述

Ethylmalonic acid can be found in blood, cerebrospinal fluid (CSF), and urine, as well as in human fibroblasts, prostate, and skeletal muscle tissues. Moreover, ethylmalonic acid is found to be associated with anorexia nervosa and malonyl-CoA decarboxylase deficiency. Ethylmalonic acid is a non-carcinogenic potentially toxic compound. Chronically high levels of ethylmalonic acid are associated with at least two inborn errors of metabolism, including short chain acyl CoA dehydrogenase deficiency (SCAD deficiency) and ethylmalonic encephalopathy.

Cas No.

601-75-2

分子式

C5H8O4

分子量

132.115

别名

乙基丙二酸;2-Ethylmalonic acid;alpha-Carboxybutyrate;Ethylmalonic acid

储存和溶解度

H2O:10 mM
Powder: -20°C for 3 years
In solvent: -80°C for 2 years