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H-HoPro-OH
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
H-HoPro-OH图片
CAS NO:3105-95-1
包装:100mg
市场价:625元

产品介绍
H-HoPro-OH (H-HoPro-OH) 是赖氨酸的分解产物,积聚在患有全身性遗传性过氧化物酶体疾病的婴儿的体液中,例如 Zellweger 综合征、新生儿肾上腺脑白质营养不良。
Cas No.3105-95-1
别名L-2-哌啶酸,H-HoPro-OH
Canonical SMILESO=C([C@H]1NCCCC1)O
分子式C6H11NO2
分子量129.16
溶解度Water: 100 mg/mL (774.23 mM); DMSO: 1 mg/mL (7.74 mM; ultrasonic and warming and heat to 80℃)
储存条件Store at -20°C
General tipsFor obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while.
Shipping ConditionEvaluation sample solution : ship with blue ice
All other available size: ship with RT , or blue ice upon request
产品描述

H-HoPro-OH is a breakdown product of lysine, accumulates in body fluids of infants with generalized genetic peroxisomal disorders, such as Zellweger syndrome, neonatal adrenoleukodystrophy.

[1]. Mihalik SJ, et al. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. Pediatr Res. 1989 May;25(5):548-52.