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Tiglyl carnitine
本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。
Tiglyl carnitine图片
CAS NO:64681-36-3
包装与价格：
包装价格(元)
1mg电议
5mg电议

产品介绍
Tiglylcarnitine被发现和乳糜泻，线粒体乙酰辅酶A硫代酶(T2)缺乏症有关。
Cas No.64681-36-3
Canonical SMILESC/C=C(C)/C(O[C@H](CC([O-])=O)C[N+](C)(C)C)=O
分子式C12H21NO4
分子量243.3
溶解度Soluble in DMSO
储存条件Store at -20°C
General tipsFor obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while.
Shipping ConditionEvaluation sample solution : ship with blue ice
All other available size: ship with RT , or blue ice upon request
产品描述

Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

[1]. Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity. J Inherit Metab Dis. 2003;26(5):423-31.